El losartán pertenece al grupo de los inhibidores de los receptores de angiotensina II, fármacos muy utilizados en el momento actual para el tratamiento de la. Queratodermia palmoplantar epidermolítica asociada a pelo lanoso, syndrome de Ehlers Danlos y miocardiopatía dilatada. Gaceta Dermatológica Ecuatoriana. Dermatol. peru. ; 13 (2): – HIPERQUERATOSIS PALMOPLANTAR Y ENFERMEDAD PERIODONTAL: SÍNDROME DE PAPILLON – LEFÉVRE – A.

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On the other hand, atypical forms of dermatophytosis have been linked to AIDS. In addition to the marked palmoplantar keratosis, patients have scaly erythematous and circumscribed patches on the elbows, knees, forearms, shins and dorsum of the hands. Synovectomy has been shown to alleviate the inflammation associated with destructive arthritis but may lead to loss in the range of the joint motion. Subscriber If you already have your login data, please click here.

Successful periodontal maintenance of a case with Papillon-Lefevre syndrome: Acta Derm Venerol, 83pp. Destructive arthritis of the wrist and shoulder joints has hiperqueratosiss reported in isolated palmop,antar.

Dermatophyte infections cause specific humoral and cellular immune response, and the protective response against dermatophytes is mainly mediated by hypersensitivity reaction of the delayed type.

However, in immunocompromised patients, there may be greater tissue necrosis, major abscess formation and absence of granulomas.


No ectoparasites were found. SJR uses a similar algorithm as the Google page rank; it provides a quantitative and qualitative measure of the journal’s impact. Various treatment approaches to periodontal conditions associated with PLS include oral hygiene instructions, use of chlorhexidine rinses, frequent debridement, systemic antibiotic regimens, periodontal surgery, extraction of hopeless teeth and referral to dermatologists to treat hiperquerahosis lesions 11, 16, All articles are subjected to a rigorous process of revision in pairs, and careful editing for literary and scientific style.

Orphanet: Hiperqueratosis palmoplantar periodontopat a onicogriposis

We requested anti-HIV reactive and anti-HTLV non-reactive serology; the hemogram revealed leukopenia while other laboratory tests hiperqureatosis normal. Even so she had not sought treatment until age 8 years. Genetic counseling HMS is transmitted as an pqlmoplantar recessive trait. Genetic analysis of several affected families suggested that the disorder may result from mutations of a gene that regulates production of an enzyme known as Cathepsin-C CTSC.

There was a complete regression of exfoliative erythroderma and palmoplantar hyperkeratosis after 28 and 90 days, respectively. HIV patients usually have superficial mycoses in many stages of the disease.

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Continuing navigation will be considered as acceptance of this use. Clin Infect Dis, 22pp. Int J Dermatol ; There was loss of gingival stippling with bleeding occurring on probing the involved gums.

There are also multiple congenital variants, with mutated genes and chromosomal hiperquerqtosis recently discovered. Because the aetiology and pathogenesis of PLS periodontitis is directly related to high levels of A actinomycetemcomitans, the administration of an antibiotic that acts specifically on this pathogen has been claimed to be important for a successful treatment plan 16, Hiperqeratosis seven-day long course of treatment with this combination has been shown to eradicate this pathogen for up to two years following treatment in patients with chronic periodontitis and in one PLS patient The patient’s elbows and knees were not affected.


In the present case, the diagnosis of PLS was made primarily based on the clinical, radiological and dermatological features besides analysis of laboratory tests. HMS is rare with less than cases reported in the literature so far.

Genetic counseling Transmission appears to be autosomal dominant.

Summary and related texts. Palmoplantar keratoderma develops during infancy and may have an unusual pattern, affecting the two sides of fingers and palms, but usually sparing the palmar sides. A scalp biopsy revealed follicular fungal invasion and Majocchi’s granuloma.

Based on clinical, dermatological and laboratory findings, hiperqqueratosis presumptive diagnosis of Papillon-Lefevre syndrome was made. Specialised Social Services Eurordis directory.